Inferior Vena Caval Dysgenesis (Azygous Continuation of the IVC):
Clinical:
The right subcardinal vein becomes the suprarenal portion of the IVC and joins with the intrahepatic IVC. The right supracardinal vein becomes the infrarenal segment of the IVC.Persistence of the left supracardinal vein results in a duplicated pre-renal IVC, while persistence of the right posterior cardinal vein results in the formation of a retrocaval ureter.
Failure of formation of the right subcardinal vein results in a discontiuous segment of the inferior vena cava between the level of the renal veins and the suprahepatic IVC (azygous continuation of the IVC). In this condition the hepatic veins drain directly into the right atrium via the suprahepatic IVC.
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